Dermatitis Herpetiformis - Definition, Causes, Symptoms and Treatment

Dermatitis herpetiformis (DH) is a skin disorder oftengluten (a protein found in cereals) sensitivity in the small
associated with celiac disease. (DH) is an intenselybowel. This means that instead of being highly
itchy skin eruption. Dermatitis herpetiformis usuallyconvoluted, the lining of the intestines is smooth and
begins in persons age 20 and older, although childrenflattened. Gluten is a protein present in grasses of the
may sometimes be affected. It is seen in both menspecies Triticeae, which includes barley, rye, and
and women. It usually shows up in young adults, and iswheat. Rice and oats belong to different species and
more common in men and people originally from someare generally well tolerated. Hormonal factors may
areas of northern Europe. It has been hypothesizedalso play a role in the pathogenesis of DH. Androgens
that DH is the result of an immunologic response tohave a suppressive effect on immune activity, including
chronic stimulation of the gut mucosa by dietary glutendecreased autoimmunity, and androgen deficient
with subsequent activation of cutaneous endothelialstates may be a potential trigger for DH exacerbation.
cells and circulating inflammatory cells, includingIgA circulating immune complexes are present in
neutrophils. DH was formerly described in the literature25-35% of patients with DH, although no association
as Duhring's Disease. Several chemicals have beenwith disease severity has been noted. These immune
associated with induction of DH, including potassiumcomplexes also have been noted in patients with
iodide and cleaning solutions. It has a typical onset in theisolated GSE and are believed to be related to the
teens or in the third or fourth decades of life. In the U.S.,presence of the gut disease. Associated autoimmune
the presence of diagnosed cases is estimated to bediseases include dermatomyositis, type 1 diabetes
about 1 in 10,000 with a male/female ratio of 2:1. It ismellitus, myasthenia gravis, rheumatoid arthritis,
more common in whites and rare in people of AfricanSjögren syndrome, systemic lupus
or Asian descent. If you have DH, you always haveerythematosus, and thyroid abnormalities. Thyroid
gluten intolerance. With DH, the primary lesion is on theabnormalities are present in as many as 50% of DH
skin, whereas with celiac disease the lesions are in thepatients and include hypothyroidism, hyperthyroidism,
small intestine.thyroid nodules, and thyroid cancer.Gastric manipulation
Symptoms of dermatitis herpetiformis are intense(surgery) may induce DH.
burning, stinging and itching around the elbows, knees,There is a very effective treatment available for
scalp, buttocks and back. More locations can also bedermatitis herpetiformis. A gluten-free diet is very
affected and the severity can vary. Scratching willdifficult to achieve; however, limiting intake of wheat,
further irritate the eruptions. Eruptions commonly occurbarley, or rye products can lessen the symptoms.
on pressure points, such as around the elbows, theDapsone can be associated with severe hematologic
front of the knees, the buttocks, back face, and scalp(blood) disturbances and must be closely monitored.
but can appear anywhere on the body. Eruptions areHowever, strict long-term avoidance of dietary gluten
usually bilateral - occurring on both sides of the body.has been shown to reduce the dose of dapsone
Ingestion of gluten plays a role in the exacerbation ofrequired to control the disease and may even eliminate
skin lesions. Small blisters usually develop gradually,the need for medication. In addition, a gluten-free diet
mostly on the elbows, knees, buttocks, lower back, andmay reduce the risk of gastrointestinal lymphoma.
back of the head. Sometimes blisters break out on theOther, less effective treatments for DH include
face and neck. The rash may be small lumps, likecolchicine, cyclosporine, azathioprine, and prednisone.
insect bites (papules), some with tiny fluid filled blistersUV light may provide some symptomatic relief.
on top. These small blisters are called vesicles.Cyclosporine should be used with caution in patients
However it can also appear hive-like, persisting in onewith DH because of a potential increase in the risk of
area, or it may look like a pink and scaly dermatitis. Thedeveloping intestinal lymphomas. Nonsteroidal
fact that the rash is most prevalent at pressure pointsanti-inflammatory drugs may exacerbate DH; however,
(where clothing rubs the most) may be why theibuprofen appears to be safe. Gulphapyridine or
symptoms sometimes appear to be symmetrical.sulphamethoxypyridazine have been used to suppress
Typically, the onset of DH is in the second to fourththe skin manifestation. It takes several months for the
decade; however, persons of any age may beskin to improve on these drugs and they do not
affected.protect against the serious complication of gluten
Dermatitis herpetiformis is frequently associated withhypersensitivity.